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Pancreatic Neuroendocrine Tumors (PNET)

Pancreatic Cancer

Overview

PNETs are rare, may be functional (hormone-secreting) or non-functional.

Symptoms

  • Hypoglycemia (insulinoma)
  • Ulcers (gastrinoma)
  • Abdominal pain
  • Weight loss

Diagnosis

  • Chromogranin A
  • CT/MRI
  • EUS
  • Ga-68 DOTATATE PET

Treatments

  • Surgical resection
  • Somatostatin analogs
  • Everolimus
  • PRRT

Risk Factors

⚠️MEN1
⚠️VHL
⚠️NF1

Key Facts

  • ℹ️<5% of pancreatic tumors
  • ℹ️Better prognosis than PDAC

ICD-10: C25.4 | Prevalence: nadir

Last updated: 11/9/2025

Pankreatik Nöroendokrin Tümörler (PNET): Belirtiler ve Tedavi