Back to Articles

Sickle Cell Disease

Hematologic Disorder

Overview

Sickle cell disease is inherited hemoglobinopathy causing RBC sickling, vaso-occlusion, hemolysis.

Symptoms

  • Pain crises
  • Anemia
  • Dactylitis
  • Stroke

Diagnosis

  • HbS on electrophoresis
  • Newborn screening
  • CBC (low Hb, high retic)

Treatments

  • Hydroxyurea
  • Transfusion
  • Pain management
  • BMT (cure)

Risk Factors

⚠️African descent
⚠️Family history

Key Facts

  • ℹ️1 in 365 African Americans
  • ℹ️SCD complications: ACS, splenic sequestration

ICD-10: D57 | Prevalence: yaygın (endemik)

Last updated: 11/9/2025

Orak Hücre Hastalığı: Belirtiler ve Tedavi